A rare case of fibrous dysplasia in the mandible: a case report

Fibrous Dysplasia in the Mandible

Authors

Keywords:

Fibrous dysplasia, Mandible, Magnetic resonance imaging

Abstract

Background: Fibrous dysplasia (FD) is a benign fibro-osseous lesion of the bone which can be monostotic FD and the polyostotic form. Polyostotic FD with café-au-lait spots of the skin and hormonal imbalances is called McCune–Albright syndrome. Besides, Mazabraud syndrome is characterized by polyostotic FD and intramuscular myxomas. FD has its onset during childhood or early adolescence and usually occurs within the first or second decade of life.

The mode of presentation of the FD of the jaw ranges from asymptomatic to dental anomalies, pain, and facial asymmetry. Given the clinical history and radiological assessment, cystic lesions have some important differential diagnoses which range from cystic ameloblastoma, fibrous dysplasia, aneurysmal bone cyst, and odontogenic keratocyst.

Case report: This presents a 19-year-old female who presented to the maxillofacial surgeons’ clinic with a referral from a peripheral hospital. Her major complaint was right-sided facial swelling which was noticed 4 years before the presentation. A plain radiograph revealed an expansile lesion of the mid-right mandible appearing as a well-outlined, fairly oval multiloculated cystic radiolucent mass with multiple internal septations. A preliminary diagnosis of a complex cystic right jaw mass with benign features was made with possible differential diagnoses such as ameloblastoma, fibrous dysplasia, aneurysmal bone cyst, and odontogenic keratocyst were suggested as possible differential diagnoses. Finally, she had an excision biopsy with a histological diagnosis of fibrous dysplasia. The outcome of the surgery was satisfactory at one year review.

 

Author Biographies

Samson Emeka OBIRIJA

Department of Radiology, Alex Ekwueme Federal University Teaching Hospital, Abakaliki Ebonyi State,

Mumini Wemimo RASHEED

Department of Anatomic Pathology, College of Medicine and Allied Medical Science, Federal University Dutse, Jigawa State, Nigeria,

Juliet Ebele OKONKWO

Department of Radiology, Lagos University Teaching Hospital, Idi-Araba, Lagos State, Nigeria

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Published

2024-02-26